Rhabdomyosarcoma

Findings:
Axial and coronal contrast enhanced  CT demonstrates a heterogenous strongly enhancing mass originating from the right masticator space, with skull base invasion and intracranial extent. The skull base foramina are destroyed in this region, but the tumor may have extended through the foramen ovale initially. Coronal and axial enhanced T1 images show the enhancing mass with infiltration of the right pterygoid muscles.

Differential Diagnosis:
Masticator space tumors include sarcomas (chondro-, rhabdo-, osteo-), squamous cell carcinoma extension from oropharynx, lymphoma, schwannoma, and metastasis.

Discussion:
Since the primary components of the masticator space include muscles (mastication) , bone (mandible), and cartilage (TMJ), sarcomas are relatively common in this location. Rhabdomyosarcoma is most commonly seen in patients less than 10 years old, and has a propensity for skull base invasion if it involves the nasopharynx or masticator space. The tumor may be hemorrhagic. Response to chemotherapy and radiation may be favorable, but the five year survival rate is less than 50% overall. Rhabdomyosarcomas comprise approximately 10% of malignancies in patients less than 15 years old.

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